Diseases

Klippel-Trenaunay-Weber Syndrome (Congenital Bronchiectasia)

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Klippel-trenaunay-weber syndrome (ktws) is characterized by a triad of port-wine stain, varicose veins, and bony and soft tissue hypertrophy involving an extremity. Note the image below. Klippel-trenaunay syndrome in a young person. Note the port-wine stain extending to the buttocks.

SYMPTOMS

Klippel-trenaunay-weber (ktw) syndrome is a condition characterized by a triad of findings: port-wine stain or "birthmark" (capillary malformations in the skin) soft tissue and bony hypertrophy (excessive growth of the soft tissue and/or bones) most often involving a single limb.

CAUSES

Klippel-trenaunay syndrome is a condition that affects the development of blood vessels, soft tissues (such as skin and muscles), and bones. The disorder has three characteristic features: a red birthmark called aport-wine stain, abnormal overgrowth of soft tissues and bones, and vein malformations.